- Section 1 Basic instrumentation and modalities
- Section 2 Cardiac morphology, haemodynamics, and physiology
- Section 3 Echocardiographic assessment of disease
- Chapter 25 Heart failure: left ventricular systolic dysfunction
- Chapter 26 Heart failure: left ventricular dyssynchrony
- Chapter 27 Heart failure: risk stratification and follow-up
- Chapter 28 Heart failure: preserved left ventricular ejection fraction
- Chapter 29 Ischaemic heart disease: acute coronary syndrome
- Chapter 30 Ischaemic heart disease: coronary artery anomalies
- Chapter 31 Heart valve disease (aortic valve disease): anatomy and pathology of the aortic valve
- Chapter 32 Heart valve disease (aortic valve disease): aortic stenosis
- Chapter 33 Heart valve disease (aortic valve disease): aortic regurgitation
- Chapter 34 Heart valve disease (mitral valve disease): anatomy and morphology of the mitral valve
- Chapter 35 Heart valve disease (mitral valve disease): mitral stenosis
- Chapter 36 Heart valve disease (mitral valve disease): mitral regurgitation
- Chapter 37 Heart valve disease: tricuspid valve disease
- Chapter 38 Heart valve disease: pulmonary valve disease
- Chapter 39 Heart valve disease: mixed valve disease, multiple valve disease, and others
- Chapter 40 Replacement heart valves
- Chapter 41 Endocarditis
- Chapter 42 Hypertrophic cardiomyopathy
- Chapter 43 Dilated cardiomyopathy
- Chapter 44 Restrictive cardiomyopathy and arrhythmogenic right ventricular cardiomyopathy
- Chapter 45 Isolated ventricular non-compaction
- Chapter 46 Takotsubo syndrome
- Chapter 47 Familial cardiomyopathies
- Chapter 48 Right ventricular dilatation and function
- Chapter 49 Pericardial disease
- Section 4 Echocardiographic assessment of disease
- Section 5 Specific clinical context/environment
- Section 6 Miscellaneous topics
(p. 386) Restrictive cardiomyopathy and arrhythmogenic right ventricular cardiomyopathy
- Chapter:
- (p. 386) Restrictive cardiomyopathy and arrhythmogenic right ventricular cardiomyopathy
- Author(s):
Perry Elliott
, Kristina H. Haugaa
, Pio Caso
, and Maja Cikes
- DOI:
- 10.1093/med/9780198726012.003.0044
Restrictive cardiomyopathy is a heart muscle disorder characterized by increased myocardial stiffness that results in an abnormally steep rise in intraventricular pressure with small increases in volume in the presence of normal or decreased diastolic left ventricular volumes and normal ventricular wall thickness. The disease may be caused by mutations in a number of genes or myocardial infiltration. Arrhythmogenic right ventricular cardiomyopathy is an inherited cardiac muscle disease associated with sudden cardiac death, ventricular arrhythmias, and cardiac failure. It is most frequently caused by mutations in desmosomal protein genes that lead to fibrofatty replacement of cardiomyocytes, right ventricular dilatation, and aneurysm formation.
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- Section 1 Basic instrumentation and modalities
- Section 2 Cardiac morphology, haemodynamics, and physiology
- Section 3 Echocardiographic assessment of disease
- Chapter 25 Heart failure: left ventricular systolic dysfunction
- Chapter 26 Heart failure: left ventricular dyssynchrony
- Chapter 27 Heart failure: risk stratification and follow-up
- Chapter 28 Heart failure: preserved left ventricular ejection fraction
- Chapter 29 Ischaemic heart disease: acute coronary syndrome
- Chapter 30 Ischaemic heart disease: coronary artery anomalies
- Chapter 31 Heart valve disease (aortic valve disease): anatomy and pathology of the aortic valve
- Chapter 32 Heart valve disease (aortic valve disease): aortic stenosis
- Chapter 33 Heart valve disease (aortic valve disease): aortic regurgitation
- Chapter 34 Heart valve disease (mitral valve disease): anatomy and morphology of the mitral valve
- Chapter 35 Heart valve disease (mitral valve disease): mitral stenosis
- Chapter 36 Heart valve disease (mitral valve disease): mitral regurgitation
- Chapter 37 Heart valve disease: tricuspid valve disease
- Chapter 38 Heart valve disease: pulmonary valve disease
- Chapter 39 Heart valve disease: mixed valve disease, multiple valve disease, and others
- Chapter 40 Replacement heart valves
- Chapter 41 Endocarditis
- Chapter 42 Hypertrophic cardiomyopathy
- Chapter 43 Dilated cardiomyopathy
- Chapter 44 Restrictive cardiomyopathy and arrhythmogenic right ventricular cardiomyopathy
- Chapter 45 Isolated ventricular non-compaction
- Chapter 46 Takotsubo syndrome
- Chapter 47 Familial cardiomyopathies
- Chapter 48 Right ventricular dilatation and function
- Chapter 49 Pericardial disease
- Section 4 Echocardiographic assessment of disease
- Section 5 Specific clinical context/environment
- Section 6 Miscellaneous topics